Abstract:
Hemophilia is the condition in which the blood clots very slowly and in severe cases spontaneous
bleeding into muscles and joints. It is genetic disorder caused primarily by a deficiency of
important coagulation or clotting factors. The purpose of this project based thesis was to
determine the prevalence of hemophilia cases over the past ten years among patients visiting
Black Lion Hospital. Retrospective study was conducted by using all the available secondary
data from the patients’ record in Black Lion Hospital. Descriptive statistics was employed to
determine the frequency of Hemophilia A and Hemophilia B and their relative frequencies over
ten years. The relevant data was analyzed using SPSS software window16. Over the past ten
years, a total of 153 patients medical records were found and all of which were for males. The
medical records indicated that all patients were males and no female patients, revealing that the
disorder is genetical and fulfilling the conditions for X-linked traits and disorders. From 153
male patients’ medical record, 147 of them had hemophilia A and only 6 of them were with
hemophilia B. On the bases of Ethiopia age structure, the finding also revealed that hemophilia
A within the age group of 0-14 was 0.003% and for the age group 15-64 was 0.001%, while
hemophilia B within the age group 0-14 was 0.00006 % and for the age group 15-64 was
0.0001%. Their medical records also revealed that none of the patients were aged above 64 or
no patient aged above 64 was treated in the hospital on hemophilia cases. Relatively more
hemophilia A cases were recorded between 2008-2012 while between 2003 -2007 hemophilia A cases were low. On the other hand, no hemophilia B cases were found in the year 2004, 2005,
2009 and 2012 while in all the remaining years only one case per year was recorded. Finally
based on the above findings it can be suggested that the hospital has to home care treatment and
prepare or look for more factor VIII than IX. Awareness creation for patients as well as the
community must be made to know their medical history so as to save the next generation as
hemophilia is sex linked genetic disorder.